ekonsil-logo


Johnson Munson syndrome

ICD-9 Search for Johnson Munson syndrome




Go to comments for Johnson Munson syndrome



Aphalangy, hemivertebrae and urogenital-intestinal dysgenesis is an extremely rare syndrome, described only in three siblings[1]. It associates hypoplasia or aplasia of phalanges of hands and feet, hemivertebrae and various urogenital and/or intestinal abnormalities. Intrafamilial variability is important as one sister had lethal abnormalities (Potter syndrome and pulmonary hypoplasia), while her affected brother was in good health with normal psychomotor development at 6 months of age. Prognosis seems to depend mainly on the severity of visceral malformations. Etiology and inheritance remain unknown.[2][3]






Next Page   |   Top



This article is based on an article from Wikipedia, the free encyclopedia and is available under the terms of GNU Free Documentation License.



In the Wikipedia there is a list with all authors of this article available.


Add Comment / Question


Comments for Johnson Munson syndrome:

No Comments found for Johnson Munson syndrome